Management of Duodenal Atresia in the setting of Congenital Leukemia with Massive Hepatomegaly
نویسنده
چکیده
Down's syndrome (DS) is associated with duodenal atresia (DA) in about 8-10% of cases. Transient Myeloproliferative Disorder (TMD)/Acute Myeloid Leukemia (AML) is also associated with the trisomy 21 mutation. The occurrence of the two conditions together complicates the diagnosis and surgical management of the DA. We discuss the technical aspects of management of the DA in this clinical setting.
منابع مشابه
A Retrospective Analysis of Duodenal and Jejunointestinal Atresia-Five-Year Experience from a Tertiary Care Paediatric Surgery Center in Western India.
Background: Intestinal atresia is a life-threatening problem requiring early active intervention. The aim of the study was to compare management outcomes between Duodenal-Atresia (DA) and Jejunoileal-Atresias (JIA). The secondary objective was to analyse tapering enteroplasty versus end-to-end anastomosis in JIA. Materials and Methods: Retrospective descriptive analysis of patients operated be...
متن کاملCMV-induced Duodenal Papillitis in a Child with Acute Lymphoblastic Leukemia
This article has no abstract.
متن کاملCongenital neuroblastoma presented with cholestasis and huge hepatomegaly
This case report is about a 28-day-old neonate that had abdominal distention and massive hepatomegaly since 15th days of birth. First, he was normal, and he had not any sign and symptom of sepsis. At admission, he was about twelve days, he had a rapid progressive presentation of sepsis and unfortunately, he passed away. His liver biopsies manifested the neuroblastoma.
متن کاملMassive hepatomegaly in 99mTc-octreotide scintigraphy: The value of 99mTc-sulfur colloid scan
99mTc-octreotide scintigraphy, performed during the following up a 58-year old man with neuroendocrine tumor demonstrated massive hepatomegaly demonstrating multiple areas of increased and decreased uptake. Due to severe hepatomegaly concurrence of any other abdominal soft tissue lesions could not be excluded. A 99mTc-sulfur colloid scan was done and thoroughly compared wi...
متن کاملDuodenal Atresia
(This section is meant for residents to check their understanding regarding a particular topic) QUESTIONS 1. Briefly describe embryogenesis of duo-denal atresia 2. How duodenal atresia is classified? 3. What anomalies are associated with du-odenal atresia? 4. Discuss the role of antenatal ultrasound in babies with duodenal atresia 5. What are the important clinical features of duodenal atresia?...
متن کامل